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A case of severe glutathione synthetase deficiency with novel GSS mutations

Glutathione synthetase deficiency (GSSD) is a rare inborn error of glutathione metabolism with autosomal recessive inheritance. The severe form of the disease is characterized by acute metabolic acidosis, usually present in the neonatal period with hemolytic anemia and progressive encephalopathy. A...

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Bibliografiske detaljer
Udgivet i:Braz J Med Biol Res
Main Authors: Xia, H., Ye, J., Wang, L., Zhu, J., He, Z.
Format: Artigo
Sprog:Inglês
Udgivet: Associação Brasileira de Divulgação Científica 2018
Fag:
Online adgang:https://ncbi.nlm.nih.gov/pmc/articles/PMC5769757/
https://ncbi.nlm.nih.gov/pubmed/29340523
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1590/1414-431X20176853
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