A carregar...

Ten-year-long enzyme replacement therapy shows a poor effect in alleviating giant leg ulcers in a male with Fabry disease

Fabry disease is an X-linked lysosomal storage disorder caused by a deficiency of α-galactosidase A (α-gal A), leading to the progressive accumulation of glycosphingolipids. Classical hemizygous males usually present symptoms, including pain and paresthesia in the extremities, angiokeratoma, hypo- o...

ver descrição completa

Na minha lista:
Detalhes bibliográficos
Publicado no:Mol Genet Metab Rep
Main Authors: Okada, Jun, Hossain, Mohammad Arif, Wu, Chen, Miyajima, Takashi, Yanagisawa, Hiroko, Akiyama, Keiko, Eto, Yoshikatsu
Formato: Artigo
Idioma:Inglês
Publicado em: Elsevier 2017
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5758919/
https://ncbi.nlm.nih.gov/pubmed/29326878
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ymgmr.2017.12.004
Tags: Adicionar Tag
Sem tags, seja o primeiro a adicionar uma tag!