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The prevalence of DICER1 pathogenic variation in population databases

The DICER1 syndrome is associated with a variety of rare benign and malignant tumors, including pleuropulmonary blastoma (PPB), cystic nephroma (CN) and Sertoli-Leydig cell tumor (SLCT). The prevalence and penetrance of pathogenic DICER1 variation in the general population is unknown. We examined th...

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Pubblicato in:Int J Cancer
Autori principali: Kim, Jung, Field, Amanda, Schultz, Kris Ann P., Hill, D. Ashley, Stewart, Douglas R.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2017
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5749397/
https://ncbi.nlm.nih.gov/pubmed/28748527
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/ijc.30907
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