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Periodontitis in Chédiak-Higashi Syndrome: An Altered Immunoinflammatory Response

Chédiak-Higashi syndrome (CHS), a rare autosomal recessive disorder caused by mutations in the lysosomal trafficking regulator gene (LYST), is associated with aggressive periodontitis. It is suggested that LYST mutations affect the toll-like receptor (TLR)–mediated immunoinflammatory response, leadi...

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Publicat a:JDR Clin Trans Res
Autors principals: Thumbigere Math, V., Rebouças, P., Giovani, P.A., Puppin-Rontani, R.M., Casarin, R., Martins, L., Wang, L., Krzewski, K., Introne, W.J., Somerman, M.J., Nociti, F.H., Kantovitz, K.R.
Format: Artigo
Idioma:Inglês
Publicat: SAGE Publications 2017
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5734460/
https://ncbi.nlm.nih.gov/pubmed/29276776
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1177/2380084417724117
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