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Bacterial infections in patients with primary ciliary dyskinesia: Comparison with cystic fibrosis

Primary ciliary dyskinesia (PCD) is an autosomal recessive disorder associated with severely impaired mucociliary clearance caused by defects in ciliary structure and function. Although recurrent bacterial infection of the respiratory tract is one of the major clinical features of this disease, PCD...

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Detalles Bibliográficos
Publicado en:Chron Respir Dis
Main Authors: Wijers, Christiaan DM, Chmiel, James F, Gaston, Benjamin M
Formato: Artigo
Idioma:Inglês
Publicado: SAGE Publications 2017
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC5729729/
https://ncbi.nlm.nih.gov/pubmed/29081265
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1177/1479972317694621
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