Lymphadenopathy driven by TCR-V(γ)8V(δ)1 T-cell expansion in FAS-related autoimmune lymphoproliferative syndrome

FAS-dependent apoptosis in V(δ)1 T cells makes the latter possible culprits for the lymphadenopathy observed in patients with FAS mutations. Rapamycin and methylprednisolone resistance should prompt clinicians to look for V(δ)1 T cell proliferation in ALPS-FAS patients.

Wedi'i Gadw mewn:
Manylion Llyfryddiaeth
Cyhoeddwyd yn:Blood Adv
Prif Awduron: Vavassori, Stefano, Galson, Jacob D., Trück, Johannes, van den Berg, Anke, Tamminga, Rienk Y. J., Magerus-Chatinet, Aude, Pellé, Olivier, Camenisch Gross, Ulrike, Marques Maggio, Ewerton, Prader, Seraina, Opitz, Lennart, Nüesch, Ursina, Mauracher, Andrea, Volkmer, Benjamin, Speer, Oliver, Suda, Luzia, Röthlisberger, Benno, Zimmermann, Dieter Robert, Müller, Rouven, Diepstra, Arjan, Visser, Lydia, Haralambieva, Eugenia, Neven, Bénédicte, Rieux-Laucat, Frédéric, Pachlopnik Schmid, Jana
Fformat: Artigo
Iaith:Inglês
Cyhoeddwyd: American Society of Hematology 2017
Pynciau:
Exceptional Case Report
Mynediad Ar-lein:https://ncbi.nlm.nih.gov/pmc/articles/PMC5728321/
https://ncbi.nlm.nih.gov/pubmed/29296752
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1182/bloodadvances.2017006411
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