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Clinical and Radiographic Features of Pycnodysostosis with Emphasis on Dentofacial Problems

Pycnodysostosis (PDO) is a rare genetic disorder characterized by cathepsin K deficiency which plays an important role in bone metabolism. Among clinical features of this disease which are mainly caused by altered bone remodeling are craniofacial abnormalities such as hypoplastic maxilla and obtuse...

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Publicat a:Case Rep Dent
Autors principals: Aghili, Hossein, Tabatabaei, Seyed Mohammad Ali, Goldani Moghadam, Mahdjoube
Format: Artigo
Idioma:Inglês
Publicat: Hindawi 2017
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5727649/
https://ncbi.nlm.nih.gov/pubmed/29318055
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2017/4352485
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