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Distinct functional consequences of ECEL1/DINE missense mutations in the pathogenesis of congenital contracture disorders

Endothelin-converting enzyme-like 1 (ECEL1, also termed DINE in rodents), a membrane-bound metalloprotease, has been identified as a gene responsible for distal arthrogryposis (DA). ECEL1-mutated DA is generally characterized by ocular phenotypes in addition to the congenital limb contractures that...

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Bibliografiske detaljer
Udgivet i:Acta Neuropathol Commun
Main Authors: Nagata, Kenichi, Takahashi, Mika, Kiryu-Seo, Sumiko, Kiyama, Hiroshi, Saido, Takaomi C.
Format: Artigo
Sprog:Inglês
Udgivet: BioMed Central 2017
Fag:
Online adgang:https://ncbi.nlm.nih.gov/pmc/articles/PMC5683451/
https://ncbi.nlm.nih.gov/pubmed/29132416
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s40478-017-0486-9
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