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Maffucci Syndrome Associated With Adrenocorticotropic Hormone–Independent Bilateral Macronodular Adrenal Hyperplasia

CONTEXT: Maffucci syndrome is a rare, nonhereditary, mesodermal dysplastic disease characterized by the presence of multiple hemangiomas and enchondromas. This pathological condition, which is often unrecognized, is associated with a high prevalence of benign and malignant endocrine tumors involving...

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Pubblicato in:J Endocr Soc
Autori principali: Tricò, Domenico, Battaglia, Eliana, Bernini, Giampaolo
Natura: Artigo
Lingua:Inglês
Pubblicazione: Endocrine Society 2017
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5677212/
https://ncbi.nlm.nih.gov/pubmed/29264445
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1210/js.2016-1018
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