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Birt-Hogg-Dubé syndrome: awareness is important!

Birt-Hogg-Dubé (BHD) is a rare syndrome of inherited renal cell carcinomas, characterised by cutaneous lesions and pulmonary cysts and pneumothorax in a vast majority of the patients. Awareness of this syndrome is important in order to refer patients for genetic counselling and personalised follow-u...

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Dettagli Bibliografici
Pubblicato in:BMJ Case Rep
Autori principali: Oliveira, Rui Caetano, Tavares, Edgar, Sousa, Vítor, Figueiredo, Arnaldo
Natura: Artigo
Lingua:Inglês
Pubblicazione: BMJ Publishing Group 2017
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5665185/
https://ncbi.nlm.nih.gov/pubmed/29066638
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/bcr-2017-221022
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