A carregar...

Case Report: Ursodeoxycholic acid treatment in Niemann-Pick disease type C; clinical experience in four cases

In this case series, we demonstrate that Ursodeoxycholic acid (UDCA) improves liver dysfunction in Niemann-Pick type C (NPC) and may restore a suppressed cytochrome p450 system. NPC disease is a progressive neurodegenerative lysosomal storage disease caused by mutations in either the NPC1 or NPC2 ge...

ver descrição completa

Na minha lista:
Detalhes bibliográficos
Publicado no:Wellcome Open Res
Main Authors: Evans, William R.H., Nicoli, Elena-Raluca, Wang, Raymond Y., Movsesyan, Nina, Platt, Frances M.
Formato: Artigo
Idioma:Inglês
Publicado em: F1000Research 2017
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5649119/
https://ncbi.nlm.nih.gov/pubmed/29119141
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.12688/wellcomeopenres.11854.1
Tags: Adicionar Tag
Sem tags, seja o primeiro a adicionar uma tag!