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Impaired immune function in children and adults with Fanconi anemia

BACKGROUND: Fanconi anemia (FA) is a rare genetic disorder characterized by genome instability, bone marrow failure, and cancer predisposition. Previously, small studies have reported heterogeneous immune dysfunction in FA. PROCEDURE: We performed a detailed immunologic assessment in a large FA coho...

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Detalhes bibliográficos
Publicado no:Pediatr Blood Cancer
Main Authors: Myers, Kasiani C., Sauter, Sharon, Zhang, Xue, Bleesing, Jacob J., Davies, Stella M., Wells, Susanne I., Mehta, Parinda A., Kumar, Ashish, Marmer, Daniel, Marsh, Rebecca, Brown, Darron, Kovacic, Melinda Butsch
Formato: Artigo
Idioma:Inglês
Publicado em: 2017
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5639938/
https://ncbi.nlm.nih.gov/pubmed/28557197
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/pbc.26599
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