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Bilateral lung disease, extensive and diffuse. Diagnosis of pulmonary alveolar proteinosis by bronchoscopic cryobiopsy

Pulmonary alveolar proteinosis (PAP) is a rare disease characterized by the intra-alveolar accumulation of a proteinaceous phospholipid-laden material called surfactant. Clinically, this disease should be suspected with respiratory failure in association with a crazy paving pattern on high-resolutio...

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Detalhes bibliográficos
Publicado no:Respir Med Case Rep
Main Authors: Gando, Sebastián, Duré, Roberto, Violi, Damián, Vazquez, Bibiana, Labarca, Gonzalo, Fernandez-Bussy, Sebastián
Formato: Artigo
Idioma:Inglês
Publicado em: Elsevier 2017
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5633158/
https://ncbi.nlm.nih.gov/pubmed/29021953
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.rmcr.2017.09.010
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