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Clinical features and survival in senile systemic amyloidosis: comparison to familial transthyretin cardiomyopathy

Senile systemic amyloidosis (SSA) features cardiomyopathy resulting from amyloid deposits of wild-type transthyretin (TTR). From 1994 to 2009, 82 patients with SSA were diagnosed at our center; 79 were men (96%) and median age at diagnosis was 73.8 years (range, 59.1–86.0). Most patients (77/78) pre...

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Publicat a:Amyloid
Autors principals: Connors, L. H., Doros, G., Sam, F., Badiee, A., Seldin, D. C., Skinner, M.
Format: Artigo
Idioma:Inglês
Publicat: 2011
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5603797/
https://ncbi.nlm.nih.gov/pubmed/21838471
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3109/13506129.2011.574354059
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