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Propofol administration in patients with methylmalonic acidemia and intracellular cobalamin metabolism disorders: a review of theoretical concerns and clinical experiences in 28 patients

BACKGROUND: Methylmalonic acidemia and intracellular cobalamin metabolism disorders represent a heterogeneous group of inborn errors of metabolism. Most patients will require diagnostic and/or therapeutic procedures frequently requiring sedation or anesthetic management due to neurological and neuro...

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Bibliografski detalji
Izdano u:J Inherit Metab Dis
Glavni autori: Ktena, Yiouli P., Ramstad, Trygg, Baker, Eva H., Sloan, Jennifer L., Mannes, Andrew J., Manoli, Irini, Venditti, Charles P.
Format: Artigo
Jezik:Inglês
Izdano: 2015
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC5577977/
https://ncbi.nlm.nih.gov/pubmed/25985870
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s10545-015-9816-x
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