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Cutaneous manifestations of tuberous sclerosis complex and the paediatrician's role

Tuberous sclerosis complex (TSC) is a multisystem genetic disorder stemming from unregulated activation of the mammalian target of rapamycin (mTOR) pathway, resulting in the growth of hamartomas in multiple organs. TSC-related skin lesions often develop early in life and can be disfiguring, emotiona...

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Detalhes bibliográficos
Publicado no:Arch Dis Child
Main Authors: Cardis, Michael A, DeKlotz, Cynthia Marie Carver
Formato: Artigo
Idioma:Inglês
Publicado em: BMJ Publishing Group 2017
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5574405/
https://ncbi.nlm.nih.gov/pubmed/28351834
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/archdischild-2016-312001
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