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Phenotypes of Rapid Cystic Fibrosis Lung Disease Progression during Adolescence and Young Adulthood

Rationale: Individuals with cystic fibrosis are at risk for prolonged drops in lung function, clinically termed rapid decline, during discreet periods of the disease. Objectives: To identify phenotypes of rapid pulmonary decline and determine how these phenotypes are related to patient characteristi...

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Publicado en:Am J Respir Crit Care Med
Autores principales: Szczesniak, Rhonda D., Li, Dan, Su, Weiji, Brokamp, Cole, Pestian, John, Seid, Michael, Clancy, John P.
Formato: Artigo
Lenguaje:Inglês
Publicado: American Thoracic Society 2017
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC5564675/
https://ncbi.nlm.nih.gov/pubmed/28410569
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1164/rccm.201612-2574OC
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