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A Zebrafish Model of Human Fibrodysplasia Ossificans Progressiva
Fibrodysplasia ossificans progressiva (FOP) is a rare, autosomal dominant genetic disorder in humans characterized by explosive inflammatory response to injury leading to gradual ossification within fibrous tissues, including skeletal muscle, tendons, and ligaments. A variety of animal models are ne...
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| Pubblicato in: | Zebrafish |
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| Autori principali: | , , |
| Natura: | Artigo |
| Lingua: | Inglês |
| Pubblicazione: |
Mary Ann Liebert, Inc.
2017
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| Soggetti: | |
| Accesso online: | https://ncbi.nlm.nih.gov/pmc/articles/PMC5549805/ https://ncbi.nlm.nih.gov/pubmed/28394244 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1089/zeb.2016.1398 |
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