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Ruxolitinib treatment in an infant with JAK2+ polycythaemia vera-associated Budd-Chiari syndrome

Budd-Chiari syndrome (BCS) is caused by hepatic venous outflow obstruction commonly seen with myeloproliferative neoplasms (MPNs). Polycythaemia vera (PV) is a very rare MPN in childhood. This is the youngest reported patient diagnosed with PV and BCS secondary to JAK V617F mutation. A 26-month-old...

Täydet tiedot

Tallennettuna:
Bibliografiset tiedot
Julkaisussa:BMJ Case Rep
Päätekijät: Coskun, Mehmet Enes, Height, Sue, Dhawan, Anil, Hadzic, Nedim
Aineistotyyppi: Artigo
Kieli:Inglês
Julkaistu: BMJ Publishing Group 2017
Aiheet:
Linkit:https://ncbi.nlm.nih.gov/pmc/articles/PMC5535054/
https://ncbi.nlm.nih.gov/pubmed/28710306
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/bcr-2017-220377
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