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Neuro-Otological and Peripheral Nerve Involvement in Fabry Disease

Fabry disease (FD) is an X-linked lysosomal storage disease, with multisystemic glycosphingolipids deposits. Neuro-otological involvement leading to hearing loss and vestibular dysfunctions has been described, but there is limited information about the frequency, site of lesion, or the relationship...

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Опубликовано в: :Audiol Res
Главные авторы: Carmona, Sergio, Weinschelbaum, Romina, Pardal, Ana, Marchesoni, Cintia, Zuberbuhler, Paz, Acosta, Patricia, Cáceres, Guillermo, Kisinovsky, Isaac, Bayón, Luciana, Reisin, Ricardo
Формат: Artigo
Язык:Inglês
Опубликовано: PAGEPress Publications, Pavia, Italy 2017
Предметы:
Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC5534773/
https://ncbi.nlm.nih.gov/pubmed/28794847
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4081/audiores.2017.176
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