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Adult Onset Cystic Fibrosis Liver Disease: Diagnosis and characterization of an underappreciated entity

BACKGROUND & AIMS: Cystic fibrosis liver disease (CFLD), a leading cause of death in cystic fibrosis (CF), is mostly described in pediatric populations. Adult-onset CFLD lacks sufficient characterization and diagnostic tools. METHODS: A cohort of CF patients without CFLD during childhood were fo...

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Détails bibliographiques
Publié dans:Hepatology
Auteurs principaux: Koh, Christopher, Sakiani, Sasan, Surana, Pallavi, Zhao, Xiongce, Eccleston, Jason, Kleiner, David E., Herion, David, Liang, T. Jake, Hoofnagle, Jay H., Chernick, Milica, Heller, Theo
Format: Artigo
Langue:Inglês
Publié: 2017
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC5519421/
https://ncbi.nlm.nih.gov/pubmed/28422310
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/hep.29217
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