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Pyoderma Gangrenosum in a Patient with X-Linked Agammaglobulinemia

X-linked agammaglobulinemia (XLA) is a primary immunodeficiency disorder caused by germline mutations of B-cell tyrosine kinase (BTK) gene. It is characterized by decreased serum immunoglobulins levels and circulating mature B cells. This defect in humoral immunity leads to increased susceptibility...

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Detalhes bibliográficos
Publicado no:Ann Dermatol
Main Authors: Tan, Qi, Ren, Fa-liang, Wang, Hua
Formato: Artigo
Idioma:Inglês
Publicado em: The Korean Dermatological Association; The Korean Society for Investigative Dermatology 2017
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5500714/
https://ncbi.nlm.nih.gov/pubmed/28761297
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.5021/ad.2017.29.4.476
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