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Cystic Fibrosis: NHLBI Workshop on the Primary Prevention of Chronic Lung Diseases

Cystic fibrosis (CF) is a life-limiting, monogenic disorder characterized by chronic sinopulmonary and gastrointestinal involvement. Progressive pulmonary disease leads to death in the majority of patients. Despite its well-defined molecular basis related to defects in the cystic fibrosis transmembr...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:Ann Am Thorac Soc
Egile Nagusiak: Pittman, Jessica E., Cutting, Garry, Davis, Stephanie D., Ferkol, Thomas, Boucher, Richard
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: American Thoracic Society 2014
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC5473656/
https://ncbi.nlm.nih.gov/pubmed/24754825
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1513/AnnalsATS.201312-444LD
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