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P11.06 Metachronous adrenocortical carcinoma and gliosarcoma in patient with Li-Fraumeni Syndrome

Introdution: Li-Fraumeni Syndrome (LFS) is an cancer susceptibility condition, characterized by an autosomal dominant transmission that increases an individuals risk of developing early synchronous and metachronous primary tumors. Classic LFS is associated with the development of sarcomas, diagnosed...

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Détails bibliographiques
Publié dans:Neuro Oncol
Auteurs principaux: Guidi, M., Giunti, L.
Format: Artigo
Langue:Inglês
Publié: Oxford University Press 2017
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC5464024/
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/neuonc/nox036.350
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