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Characteristics of Pediatric vs Adult Pheochromocytomas and Paragangliomas

CONTEXT: Pheochromocytomas and paragangliomas (PPGLs) in children are often hereditary and may present with different characteristics compared with adults. Hereditary PPGLs can be separated into cluster 1 and cluster 2 tumors due to mutations impacting hypoxia and kinase receptor signaling pathways,...

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Dades bibliogràfiques
Publicat a:J Clin Endocrinol Metab
Autors principals: Pamporaki, Christina, Hamplova, Barbora, Peitzsch, Mirko, Prejbisz, Aleksander, Beuschlein, Felix, Timmers, Henri J.L.M., Fassnacht, Martin, Klink, Barbara, Lodish, Maya, Stratakis, Constantine A., Huebner, Angela, Fliedner, Stephanie, Robledo, Mercedes, Sinnott, Richard O., Januszewicz, Andrzej, Pacak, Karel, Eisenhofer, Graeme
Format: Artigo
Idioma:Inglês
Publicat: Endocrine Society 2017
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5460722/
https://ncbi.nlm.nih.gov/pubmed/28324046
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1210/jc.2016-3829
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