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The Coexistence of Multiple Myeloma-associated Amyloid Light-chain Amyloidosis and Fabry Disease in a Hemodialysis Patient

Fabry disease (FD) is an inherited lysosomal disorder caused by an X-linked α-galactosidase A deficiency. We report the case of a 50-year-old male FD patient on hemodialysis who presented with macroglossia-related speaking difficulty and gastrointestinal symptoms. An endoscopic analysis revealed mul...

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Detalhes bibliográficos
Publicado no:Intern Med
Main Authors: Taguchi, Kensei, Moriyama, Atsuo, Kodama, Goh, Nakayama, Yosuke, Fukami, Kei
Formato: Artigo
Idioma:Inglês
Publicado em: The Japanese Society of Internal Medicine 2017
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5457930/
https://ncbi.nlm.nih.gov/pubmed/28381753
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2169/internalmedicine.56.7623
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