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FASTKD1 and FASTKD4 have opposite effects on expression of specific mitochondrial RNAs, depending upon their endonuclease-like RAP domain

FASTK family proteins have been identified as regulators of mitochondrial RNA homeostasis linked to mitochondrial diseases, but much remains unknown about these proteins. We show that CRISPR-mediated disruption of FASTKD1 increases ND3 mRNA level, while disruption of FASTKD4 reduces the level of ND3...

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Detalhes bibliográficos
Publicado no:Nucleic Acids Res
Main Authors: Boehm, Erik, Zaganelli, Sofia, Maundrell, Kinsey, Jourdain, Alexis A., Thore, Stéphane, Martinou, Jean-Claude
Formato: Artigo
Idioma:Inglês
Publicado em: Oxford University Press 2017
Assuntos:
RNA
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5449608/
https://ncbi.nlm.nih.gov/pubmed/28335001
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/nar/gkx164
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