Cargando...

Progressive mitochondrial protein lysine acetylation and heart failure in a model of Friedreich’s ataxia cardiomyopathy

INTRODUCTION: The childhood heart disease of Friedreich’s Ataxia (FRDA) is characterized by hypertrophy and failure. It is caused by loss of frataxin (FXN), a mitochondrial protein involved in energy homeostasis. FRDA model hearts have increased mitochondrial protein acetylation and impaired sirtuin...

Descrición completa

Gardado en:
Detalles Bibliográficos
Publicado en:PLoS One
Main Authors: Stram, Amanda R., Wagner, Gregory R., Fogler, Brian D., Pride, P. Melanie, Hirschey, Matthew D., Payne, R. Mark
Formato: Artigo
Idioma:Inglês
Publicado: Public Library of Science 2017
Assuntos:
Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC5444842/
https://ncbi.nlm.nih.gov/pubmed/28542596
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0178354
Tags: Engadir etiqueta
Sen Etiquetas, Sexa o primeiro en etiquetar este rexistro!