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The factors affecting lipid profile in adult patients with Mucopolysaccharidosis

BACKGROUND: Mucopolysaccharidoses (MPS) are a group of rare inherited disorders characterized by abnormal accumulation of glycosaminoglycans (GAGs) within the myocytes and coronary arteries. Little is known about hyperlipidaemia as a potential cardiovascular risk factor in these patients. Baseline c...

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Detalhes bibliográficos
Publicado no:Mol Genet Metab Rep
Main Authors: Stepien, Karolina M., Stewart, Fiona J., Hendriksz, Chris J.
Formato: Artigo
Idioma:Inglês
Publicado em: Elsevier 2017
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5440760/
https://ncbi.nlm.nih.gov/pubmed/28560179
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ymgmr.2017.05.006
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