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Prion Strain Characterization of a Novel Subtype of Creutzfeldt-Jakob Disease

In 2007, we reported a patient with an atypical form of Creutzfeldt-Jakob disease (CJD) heterozygous for methionine-valine (MV) at codon 129 who showed a novel pathological prion protein (PrP(TSE)) conformation with an atypical glycoform (AG) profile and intraneuronal PrP deposition. In the present...

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Bibliografiske detaljer
Udgivet i:J Virol
Main Authors: Galeno, Roberta, Di Bari, Michele Angelo, Nonno, Romolo, Cardone, Franco, Sbriccoli, Marco, Graziano, Silvia, Ingrosso, Loredana, Fiorini, Michele, Valanzano, Angelina, Pasini, Giulia, Poleggi, Anna, Vinci, Ramona, Ladogana, Anna, Puopolo, Maria, Monaco, Salvatore, Agrimi, Umberto, Zanusso, Gianluigi, Pocchiari, Maurizio
Format: Artigo
Sprog:Inglês
Udgivet: American Society for Microbiology 2017
Fag:
Online adgang:https://ncbi.nlm.nih.gov/pmc/articles/PMC5432879/
https://ncbi.nlm.nih.gov/pubmed/28298604
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1128/JVI.02390-16
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