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Hyperimmunoglobulin E syndrome: Genetics, immunopathogenesis, clinical findings, and treatment modalities

The hyperimmunoglobulin E syndromes (HIESs) are very rare immunodeficiency syndromes with multisystem involvement, including immune system, skeleton, connective tissue, and dentition. HIES are characterized by the classic triad of high serum levels of immunoglobulin E (IgE), recurrent staphylococcal...

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Detalles Bibliográficos
Publicado en:J Res Med Sci
Autores principales: Hashemi, Hassan, Mohebbi, Masoumeh, Mehravaran, Shiva, Mazloumi, Mehdi, Jahanbani-Ardakani, Hamidreza, Abtahi, Seyed-Hossein
Formato: Artigo
Lenguaje:Inglês
Publicado: Medknow Publications & Media Pvt Ltd 2017
Materias:
Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC5426098/
https://ncbi.nlm.nih.gov/pubmed/28567072
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4103/jrms.JRMS_1050_16
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