Загрузка...

Novel Homozygous Missense Mutation in SPG20 Gene Results in Troyer Syndrome Associated with Mitochondrial Cytochrome c Oxidase Deficiency

Troyer syndrome is an autosomal recessive form of hereditary spastic paraplegia (HSP) caused by deleterious mutations in the SPG20 gene. Although the disease is associated with a loss of function mechanism of spartin, the protein encoded by SPG20, the precise pathogenesis is yet to be elucidated. Re...

Полное описание

Сохранить в:
Библиографические подробности
Опубликовано в: :JIMD Rep
Главные авторы: Spiegel, Ronen, Soiferman, Devorah, Shaag, Avraham, Shalev, Stavit, Elpeleg, Orly, Saada, Ann
Формат: Artigo
Язык:Inglês
Опубликовано: Springer Berlin Heidelberg 2016
Предметы:
Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC5413448/
https://ncbi.nlm.nih.gov/pubmed/27539578
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/8904_2016_580
Метки: Добавить метку
Нет меток, Требуется 1-ая метка записи!