Carregant...

A large inversion involving GNAS exon A/B and all exons encoding Gsα is associated with autosomal dominant pseudohypoparathyroidism type Ib (PHP1B)

Pseudohypoparathyroidism type Ib (PHP1B) is characterized primarily by resistance to parathyroid hormone (PTH) and thus hypocalcemia and hyperphosphatemia, in most case without evidence for Albright Hereditary Osteodystrophy (AHO). PHP1B is associated with epigenetic changes at one or several differ...

Descripció completa

Guardat en:
Dades bibliogràfiques
Publicat a:J Bone Miner Res
Autors principals: Grigelioniene, Giedre, Nevalainen, Pasi I., Reyes, Monica, Thiele, Susanne, Tafaj, Olta, Molinaro, Angelo, Takatani, Rieko, Ala-Houhala, Marja, Nilsson, Daniel, Eisfeldt, Jesper, Lindstrand, Anna, Kottler, Marie-Laure, Mäkitie, Outi, Jüppner, Harald
Format: Artigo
Idioma:Inglês
Publicat: 2017
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5395346/
https://ncbi.nlm.nih.gov/pubmed/28084650
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/jbmr.3083
Etiquetes: Afegir etiqueta
Sense etiquetes, Sigues el primer a etiquetar aquest registre!