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Post-translational Modifications and Protein Quality Control in Motor Neuron and Polyglutamine Diseases

Neurodegenerative diseases, including motor neuron and polyglutamine (polyQ) diseases, are a broad class of neurological disorders. These diseases are characterized by neuronal dysfunction and death, and by the accumulation of toxic aggregation-prone proteins in the forms of inclusions and micro-agg...

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Pubblicato in:Front Mol Neurosci
Autori principali: Sambataro, Fabio, Pennuto, Maria
Natura: Artigo
Lingua:Inglês
Pubblicazione: Frontiers Media S.A. 2017
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5374214/
https://ncbi.nlm.nih.gov/pubmed/28408866
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fnmol.2017.00082
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