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Atypical presentation of paroxysmal nocturnal hemoglobinuria treated by eculizumab: A case report

RATIONALE: Paroxysmal nocturnal hemoglobinuria (PNH) is a nonmalignant acquired hematopoietic stem cell disease, which can be revealed by hemolytic anemia, thromboembolism, or bonemarrow failure. Thrombosis can occur at any site, but coronary thrombosis is extremely rare. Controlled trials have demo...

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Detalles Bibliográficos
Publicado en:Medicine (Baltimore)
Main Authors: Quinquenel, Anne, Maestraggi, Quentin, Lecoq-Lafon, Carinne, Régis, Peffault de Latour, Delmer, Alain, Servettaz, Amélie
Formato: Artigo
Idioma:Inglês
Publicado: Wolters Kluwer Health 2017
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC5371474/
https://ncbi.nlm.nih.gov/pubmed/28328837
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/MD.0000000000006403
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