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Atypical presentation of paroxysmal nocturnal hemoglobinuria treated by eculizumab: A case report

RATIONALE: Paroxysmal nocturnal hemoglobinuria (PNH) is a nonmalignant acquired hematopoietic stem cell disease, which can be revealed by hemolytic anemia, thromboembolism, or bonemarrow failure. Thrombosis can occur at any site, but coronary thrombosis is extremely rare. Controlled trials have demo...

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Dades bibliogràfiques
Publicat a:Medicine (Baltimore)
Autors principals: Quinquenel, Anne, Maestraggi, Quentin, Lecoq-Lafon, Carinne, Régis, Peffault de Latour, Delmer, Alain, Servettaz, Amélie
Format: Artigo
Idioma:Inglês
Publicat: Wolters Kluwer Health 2017
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5371474/
https://ncbi.nlm.nih.gov/pubmed/28328837
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/MD.0000000000006403
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