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Amyloid and intracellular accumulation of BRI(2)

Familial British dementia (FBD) and familial Danish dementia (FDD) are caused by mutations in the BRI(2) gene. These diseases are characterized clinically by progressive dementia and ataxia and neuropathologically by amyloid deposits and neurofibrillary tangles. Herein, we investigate BRI(2) protein...

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Detalhes bibliográficos
Publicado no:Neurobiol Aging
Main Authors: Garringer, Holly J., Sammeta, Neeraja, Oblak, Adrian, Ghetti, Bernardino, Vidal, Ruben
Formato: Artigo
Idioma:Inglês
Publicado em: 2016
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5359036/
https://ncbi.nlm.nih.gov/pubmed/28131015
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.neurobiolaging.2016.12.018
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