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A Proposed Physiopathological Pathway to Hyperammonemic Encephalopathy in a Non-Cirrhotic Patient with Fibrolamellar Hepatocellular Carcinoma without Ornithine Transcarbamylase (OTC) Mutation

Patient: Male, 31 Final Diagnosis: Fibrolamellar hepatocellular carcinoma Symptoms: Encephalopathy Medication:— Clinical Procedure: — Specialty: Gastroenterology and Hepatology OBJECTIVE: Rare disease BACKGROUND: Hyperammonemic encephalopathy is a potentially fatal condition that may progress to irr...

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Dettagli Bibliografici
Pubblicato in:Am J Case Rep
Autori principali: Surjan, Rodrigo C., dos Santos, Elizabeth S., Basseres, Tiago, Makdissi, Fabio F., Machado, Marcel A.
Natura: Artigo
Lingua:Inglês
Pubblicazione: International Scientific Literature, Inc. 2017
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5358858/
https://ncbi.nlm.nih.gov/pubmed/28270654
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.12659/AJCR.901682
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