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Current and future therapies for inherited cholestatic liver diseases

Familial intrahepatic cholestasis (FIC) comprises a group of rare cholestatic liver diseases associated with canalicular transport defects resulting predominantly from mutations in ATP8B1, ABCB11 and ABCB4. Phenotypes range from benign recurrent intrahepatic cholestasis (BRIC), associated with recur...

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Dades bibliogràfiques
Publicat a:World J Gastroenterol
Autors principals: van der Woerd, Wendy L, Houwen, Roderick HJ, van de Graaf, Stan FJ
Format: Artigo
Idioma:Inglês
Publicat: Baishideng Publishing Group Inc 2017
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5296193/
https://ncbi.nlm.nih.gov/pubmed/28223721
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3748/wjg.v23.i5.763
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