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Current and future therapies for inherited cholestatic liver diseases

Familial intrahepatic cholestasis (FIC) comprises a group of rare cholestatic liver diseases associated with canalicular transport defects resulting predominantly from mutations in ATP8B1, ABCB11 and ABCB4. Phenotypes range from benign recurrent intrahepatic cholestasis (BRIC), associated with recur...

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Detalhes bibliográficos
Publicado no:World J Gastroenterol
Main Authors: van der Woerd, Wendy L, Houwen, Roderick HJ, van de Graaf, Stan FJ
Formato: Artigo
Idioma:Inglês
Publicado em: Baishideng Publishing Group Inc 2017
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5296193/
https://ncbi.nlm.nih.gov/pubmed/28223721
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3748/wjg.v23.i5.763
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