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Current and future therapies for inherited cholestatic liver diseases

Familial intrahepatic cholestasis (FIC) comprises a group of rare cholestatic liver diseases associated with canalicular transport defects resulting predominantly from mutations in ATP8B1, ABCB11 and ABCB4. Phenotypes range from benign recurrent intrahepatic cholestasis (BRIC), associated with recur...

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Dettagli Bibliografici
Pubblicato in:World J Gastroenterol
Autori principali: van der Woerd, Wendy L, Houwen, Roderick HJ, van de Graaf, Stan FJ
Natura: Artigo
Lingua:Inglês
Pubblicazione: Baishideng Publishing Group Inc 2017
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5296193/
https://ncbi.nlm.nih.gov/pubmed/28223721
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3748/wjg.v23.i5.763
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