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Matriptase-mediated cleavage of EpCAM destabilizes claudins and dysregulates intestinal epithelial homeostasis

Congenital tufting enteropathy (CTE) is a severe autosomal recessive human diarrheal disorder with characteristic intestinal epithelial dysplasia. CTE can be caused by mutations in genes encoding EpCAM, a putative adhesion molecule, and HAI-2, a cell surface protease inhibitor. A similar phenotype o...

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Dettagli Bibliografici
Pubblicato in:J Clin Invest
Autori principali: Wu, Chuan-Jin, Feng, Xu, Lu, Michael, Morimura, Sohshi, Udey, Mark C.
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Society for Clinical Investigation 2017
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5272188/
https://ncbi.nlm.nih.gov/pubmed/28094766
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1172/JCI88428
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