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Multifocal micronodular pneumocyte hyperplasia (MMPH) in a patient with tuberous sclerosis-evidence for long term stability

Multifocal micronodular pneumocyte hyperplasia (MMPH) is rare entity seen mostly in patients with the tuberous sclerosis complex (TSC). We present the case of a 50 year old woman with TSC (confirmed TSC2 mutation) found to have multiple ground glass opacities with an upper lobe predominance on a scr...

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Dades bibliogràfiques
Publicat a:Respir Med Case Rep
Autors principals: Pannu, Bibek S., Apala, Dinesh R., Kotecha, Aditya, Boland, Jennifer M., Iyer, Vivek N.
Format: Artigo
Idioma:Inglês
Publicat: Elsevier 2017
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5262499/
https://ncbi.nlm.nih.gov/pubmed/28149746
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.rmcr.2017.01.010
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