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Sleep-Disordered Breathing and Effects of Noninvasive Ventilation in Patients with Late-Onset Pompe Disease

STUDY OBJECTIVES: In neuromuscular disease, non-invasive ventilation (NIV) is indicated if sleep-disordered breathing (SDB) or significant respiratory muscle weakness (RMW) is present. We investigated immediate and long-term effects of NIV on sleep and nocturnal ventilation in patients with late-ons...

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Pubblicato in:J Clin Sleep Med
Autori principali: Boentert, Matthias, Dräger, Bianca, Glatz, Christian, Young, Peter
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Academy of Sleep Medicine 2016
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5155202/
https://ncbi.nlm.nih.gov/pubmed/27568896
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.5664/jcsm.6346
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