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Current Status of Dedicator of Cytokinesis-Associated Immunodeficiency: DOCK8 and DOCK2

DOCK8 deficiency is an autosomal recessive combined immunodeficiency disease associated with elevated IgE, atopy, recurrent sinopulmonary and cutaneous viral infections, and malignancy. The DOCK8 protein is critical for cytoskeletal organization, and deficiency impairs dendritic cell transmigration,...

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Detalles Bibliográficos
Publicado en:Dermatol Clin
Main Authors: Dimitrova, Dimana, Freeman, Alexandra F
Formato: Artigo
Idioma:Inglês
Publicado: 2017
Assuntos:
Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC5131797/
https://ncbi.nlm.nih.gov/pubmed/27890234
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.det.2016.07.002
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