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Identification and Functional Characterization of a Novel CACNA1C-Mediated Cardiac Disorder Characterized by Prolonged QT Intervals with Hypertrophic Cardiomyopathy, Congenital Heart Defects, and Sudden Cardiac Death

BACKGROUND: A portion of sudden cardiac deaths (SCD) can be attributed to structural heart diseases such as hypertrophic cardiomyopathy (HCM) or cardiac channelopathies such as long QT syndrome (LQTS); however, the underlying molecular mechanisms are quite distinct. Here, we identify a novel CACNA1C...

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Publicado en:Circ Arrhythm Electrophysiol
Autores principales: Boczek, Nicole J., Ye, Dan, Jin, Fang, Tester, David J., Huseby, April, Bos, J. Martijn, Johnson, Aaron J., Kanter, Ronald, Ackerman, Michael J.
Formato: Artigo
Lenguaje:Inglês
Publicado: 2015
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC5094060/
https://ncbi.nlm.nih.gov/pubmed/26253506
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1161/CIRCEP.115.002745
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