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Hermansky–Pudlak syndrome in pregnancy: A case report

Hermansky–Pudlak syndrome is a rare autosomal recessive disorder estimated to affect 1 in 500,000 to 1,000,000 individuals worldwide. Clinically, it presents as oculocutaneous albinism combined with bleeding diathesis. This is due to the absence of dense bodies in platelets causing a delayed seconda...

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Vydáno v:Obstet Med
Hlavní autoři: Yusuf, Lydia, Dukka, Srivasavi, Ciantar, Etienne
Médium: Artigo
Jazyk:Inglês
Vydáno: SAGE Publications 2016
Témata:
On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC5089347/
https://ncbi.nlm.nih.gov/pubmed/27829879
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1177/1753495X16662580
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