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The relationship between the fibrinogen D domain self-association/cross-linking site (gammaXL) and the fibrinogen Dusart abnormality (Aalpha R554C-albumin): clues to thrombophilia in the "Dusart syndrome".

Cross-linking of fibrinogen at its COOH-terminal gamma chain cross-linking site occurs in the presence of factor XIIIa due to self-association at a constitutive D domain site ("gammaXL"). We investigated the contribution of COOH-terminal regions of fibrinogen Aalpha chains to the gammaXL s...

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Dades bibliogràfiques
Publicat a:J Clin Invest
Autors principals: Mosesson, M W, Siebenlist, K R, Hainfeld, J f, Wall, J S, Soria, J, Soria, C, Caen, J P
Format: Artigo
Idioma:Inglês
Publicat: American Society for Clinical Investigation 1996
Matèries:
Accés en línia:https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC507315/
https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/8636415/
https://ncbi.nlm.nih.govhttps://doi.org/10.1172/JCI118677
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