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A Novel Mutation (S54C) of the PAX8 Gene in a Family with Congenital Hypothyroidism and High Proportion of Affected Individuals

BACKGROUND: Congenital hypothyroidism (CH) is a common endocrine disorder in newborns. The cause of CH is thyroid dysgenesis in 80%–85% of patients. Paired box gene 8 (PAX8) is a thyroid transcription factor that plays an important role in thyroid organogenesis and development. To date 22 different...

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Detalhes bibliográficos
Publicado no:Horm Res Paediatr
Main Authors: Srichomkwun, Panudda, Admoni, Osnat, Refetoff, Samuel, de Vries, Liat
Formato: Artigo
Idioma:Inglês
Publicado em: 2016
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5061635/
https://ncbi.nlm.nih.gov/pubmed/27207603
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1159/000445891
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