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FAbry STabilization indEX (FASTEX): an innovative tool for the assessment of clinical stabilization in Fabry disease

Two disease severity scoring systems, the Mainz Severity Score Index (MSSI) and Fabry Disease Severity Scoring System (DS3), have been validated for quantifying the disease burden of Fabry disease. We aimed to develop a dynamic mathematical model [the FASTEX (FAbry STabilization indEX)] to assess th...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:Clin Kidney J
Egile Nagusiak: Mignani, Renzo, Pieruzzi, Federico, Berri, Francesco, Burlina, Alessandro, Chinea, Benito, Gallieni, Maurizio, Pieroni, Maurizio, Salviati, Alessandro, Spada, Marco
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: Oxford University Press 2016
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC5036909/
https://ncbi.nlm.nih.gov/pubmed/27679722
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/ckj/sfw082
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