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Retroperitoneal fibrosis with periaortitis: A case report of an unusual form of presentation of granulomatosis with polyangiitis

Granulomatosis with polyangiitis (GPA) is the name that has been used in recent years for Wegener's granulomatosis. This condition is a systemic inflammatory disease characterised by necrotizing vasculitis that affects small and medium-sized blood vessels (capillaries, arterioles, venules and a...

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Pubblicato in:Respir Med Case Rep
Autori principali: González Revilla, Elizabeth Manuely, Fernandez, Araceli Abad, Ramirez, María Teresa Río, Pardo, Sara Calero, Moragues, María Antonia Juretschke
Natura: Artigo
Lingua:Inglês
Pubblicazione: Elsevier 2016
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5030371/
https://ncbi.nlm.nih.gov/pubmed/27672552
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.rmcr.2016.08.009
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