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Recurrent spontaneous pneumothoraces and bullous emphysema. A novel mutation causing Birt-Hogg-Dube syndrome

Birt-Hogg-Dube syndrome (BHDS) is a rare form of classically cystic lung disease that may present with spontaneous pneumothorax. The associated skin manifestations (fibrofolliculomas) are not always present. This article describes a case of spontaneous pneumothorax secondary to bullous emphysema in...

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Pubblicato in:Respir Med Case Rep
Autori principali: Burkett, Andrew, Coffey, Niamh, Tomiak, Eva, Voduc, Nha
Natura: Artigo
Lingua:Inglês
Pubblicazione: Elsevier 2016
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5018093/
https://ncbi.nlm.nih.gov/pubmed/27642565
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.rmcr.2016.08.006
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